Высокая легочная гипертензия: возможности эхокардиографии в оценке прогноза клинического течения и определении показаний к операции пересадки легких
Диссертация
Это первое исследование, в котором проанализированы различные варианты нарушения сердечной деятельности в зависимости от причин ВЛГ и функционального класса. В связи с чем, были определены эхокардиографические показатели, отражающие тяжелое клиническое течение у различных групп пациентов с BJ1I при дефеюе межжелудочковой перегородки (ДМЖП), дефекте межпредсердной перегородки (ДМПП), открытом… Читать ещё >
Содержание
- ГЛАВА. ОБЗОР ЛИТЕРАТУРЫ
- 1. 1. Классификации легочной гипертензии
- 1. 1. 1. Классификации легочной гипертензии при врожденных и приобретенных пороках сердца
- 1. 1. 2. Морфологическая классификация ПЛГ
- 1. 2. Естественное течение и выживаемость при ВЛГ
- 1. 2. 1. Больные с синдромом Эйзенменгера
- 1. 2. 2. Больные первичной легочной гипертензией
- 1. 3. Современные подходы к лечению ВЛГ
- 1. 3. 1. Консервативная терапия
- 1. 3. 2. Трансплантация легких
- 1. 4. Методы оценки морфофункционального состояния миокарда желудочков
- 1. 5. Методы оценки гемодинамики МКК
- 1. 1. Классификации легочной гипертензии
- ГЛАВА. МАТЕРИАЛ И МЕТОДЫ ИССЛЕДОВАНИЯ
- 2. 1. Краткая характеристика материала
- 2. 2. Методы исследования характеристик морфофункционалмкм о состояния сердца у больных с высокой легочной гипертензией
- 2. 3. Определение среднего давления в легочной артерии
- ГЛАВА. РЕЗУЛЬТАТЫ
- 3. 1. Показатели морфофункционального состояния сердца
- 3. 1. 2. Оценка геометрии левого желудочка у больных ВЛГ
- 3. 1. 3. Оценка диастолической функции желудочков.7()
- 3. 2. Оценка прогноза клинического течения
- 3. 2. 1. Пациенты с дефектом межжелудочковой перегородки и синдромом Эйзенменгера
- 3. 2. 2. Пациенты с высокой легочной гипертензией и интактной МЖП: ДМПП, ОАП, РВЛГ и ПЛГ
- 3. 3. Оценка эффективности гипотензивной терапии
- 3. 4. Летальные исходы
- 3. 5. Показания к операции пересадки легких
- 3. 1. Показатели морфофункционального состояния сердца
- ГЛАВА. ОБСУЖДЕНИЕ
- 4. 1. Показатели морфофункционального состояния сердца у больных с высокой легочной гипертензией (ВЛГ)
- 4. 2. Прогноз клинического течения заболевания у больных ВЛГ
- 4. 2. 1. Дефект межжелудочковой перегородки с синдромом Эйзенменгера
- 4. 2. 2. Дефект межпредсердной перегородки с синдромом Эйзенменгера
- 4. 2. 3. Пациенты с открытым артериальным протоком с синдромом Эйзенменгера
- 4. 2. 4. Больные первичной легочной гипертензией и резидуальной ВЛГ после коррекции ВГ1С. I
- 4. 3. Оценка)ффективности вазодилатирующей терапии
- 4. 4. Определение показаний к операции грансплатации лег ки
Список литературы
- Алексеевских Ю.Г. Морфологическая характеристика вторичной легочной гипертензии при циррозе печени. // Арх. патологии. 1979. — № 5. — с.38−43.
- Али Садек Али, Сергакова Л. М. Количественная оценка легочной гипертензии с помощью доптер-эхокардиографии. // Кардиология 1988. — № 7. — с.112- 15.
- Али Садек Али, Сергакова Л. М., Атьков О. Ю. //Тер. арх. -1987.- № 3.-с.38- 40.
- Беришвили И.И., Джананян В. Л., Васильев В. А. и лр. Классификация дефектов межжелудочковой перегородки. //Кардиология. 1991. — № 10. -с.61 -66.
- Ьураковский В.И., Бухарин В. А., Плотникова Л. Р. Легочная гипертензия при врожденных пороках сердца. // М., «Медицина», 1975.
- Гордиенко Б.В., Пронина В. П., Мравян С. Р., Вишняк A.M. Определение легочно-капиллярного давления у больных методом эхокардио! рафии в М-режиме. // Кардиология 1987. — № 12. — с.83- 4.
- Иваницкий А.В. с соавт. Критерии операбельности больных с общим артериальным стволом по данным гемодинамики. // Груд, и сердечнососудистая хирургия. 1991. — № 8. — с.34- 38.
- Константинова В.М. Оценка показателей гемодинамики у больных с врожденным пороком сердца и легочной гипертензией с помощью допплерэхокардиографии. //диссер. канд. мед. наук. М. 2000.
- П.Литвинов М. М., Рязанов О. Б., Чеканов B.C.: Материалы Всесоюзного симпозиума в Суздале 1991 «Экспериментальная С-С-Х».
- Пинзур С.В., Белоусов Ю. Б. Применение каптоприла при лечении хронического легочного сердца. //Клин. Мед. 1991, — № 10.- с.60−62.
- З.Плотникова Л. Р. Вопросы хирургического лечения открытого артериального протока и изолированного дефекта межжелудочковой перегородки, осложненных легочной гипертензией.: Дисс. канд. мед. наук. М., — 1968.
- Сидоренко Б.А., Преображенский Д. В. Низкомолекулярные гепарины: возможности применения. // Кардиология. 1995. — № 10. — с.86- 90.
- Федорова I А., Яблонский П. К., Александрова Н. И. Прогнозирование продолжительности жизни больных первичной легочной гипертензией. // Пульмонология. Приложение, 10. Национальный кошресс, но болезням органов дыхания. 2000. с. 134.
- Чазова И.Е. Первичная легочная гипертензия: вопросы патогенеза и дифференцированных путей лечения. //диссер. докт.мед.наук. М. 1996.
- Шиллер Н., Осипов М. А. Клиническая эхокардиография. // М., 1993.
- Школовой С.В. // Кардиология 1988ю — № 7. — с.88- 9.
- Aoyagi Т., Iizuka M., Takahashi Т., Ohya Т., Serizawa Т., Momomura S. Wall motion asynchrony prolongs time constant of left ventricular relaxation. // Am. J. Physiol. 1989. — Vol.257. — H.883- 90.
- Appleton C.P., Hatle L., Popp R.L. Relation of transmitral flow velocity patterns to left ventricular diastolic function: new insights from a combined hemodynamic and Doppler echocardiographic study. // J. Am. Coll. Cardiol.-1988, — Vol. 12, — p.426- 40.
- Appleton C.P., Hatle L.K., Popp R.L. Demonstration of restrictive ventricular physiology by Doppler echocardiography. // J. Am. Coll. Cardiol. 1988. -Vol.11. — p.757- 68.
- Arzilli F., Gandolfi E., Del Prato C. Antihypertensive effect of once daily sustained release isradipine: a placebo controlled cross over study. // Eur. J. Clin. Pharm. — 1993. — Vol.44. — p.23- 5.
- Azancot A. Candell Т., Allen H.D. et al. Echocardiographic ventricular shape analysis in congenital heart disease with right ventricular volume pressure overload. // Am. J. Cardiol. 1985. — Vol.56. — p.520- 26.
- Barst R.J., Rubin L, J" McGoon M.D., Caldwell E.J., Long W.A., Levy P. S. Survival in primary pulmonary hypertension with long-term continuous intravenous prostacyclin. // Ann. Intern. Med. 1994. — Vol.121. — p.409- 15.
- Batra А.К., Segall P.H., Ahmed T. Pulmonary edema with nifedipine in primary pulmonary hypertension. // Respiration. 1985. — Vol.47. — p. 161−3.
- Bengur A.R., Snider A.R., Vermilion R.P., Freeland J.C. Left ventricular ejection fraction measured with Doppler color flow mapping techniques. //Am. J. Cardiol. 1991. — Vol. 68. — p. 669.
- Berkenboom G., Soboliski J., Stoupel E. Failure of nifedipine treatment in primary pulmonary hypertension. // Br. Heart J. 1982. — Vol.47. — p. 511.
- Вегтап W. Jr., Wood S.C., Yabek S.M., Dillon Т., Fripp R.R., Burstein R. Systemic oxygen transport in patients with congenital heart disease. Circulation 1987, — Vol.75.- p.360- 8.
- Bing R.J., Vandam L.D., Gray F.D. Physiological stadies in congenital heart disease.// Bull. Johns Hopkins Hosp. 1947. — Vol.80. — p.323- 47.
- Birkeland S., Westby J., Hexeberg F. Grong K. l. ekven J. Compensatory regional contraction following coronary artery occlusion depends on subendocardial hyperaemia and hyperkinesis. //Eur. Heart J. 1992.- Vol. 13,-p. 1207−16.
- Bjornsson J., Edwards W.D. Primary pulmonary hypertension: a histopathologic study of 80 cases. // Mayo Clin. Proc. 1985. — Vol.60. p. 1625.
- Bommer W., Weinert L., Neumann A., Neef J., Mason D.T., DeMaria A.N. Determination of right atrial size and right ventricular size by two-dimensional echocardiography. // Circulation 1979. — Vol.60. — p. 91−100.
- Bourdillon P.D.V., Oakley C.M. Regression of primary pulmonary hypertension. // Br. Heart J.- 1976.- Vol.38.- p.264−70.
- Boxt L.M., Katz J., Kolb Т., Czegledy F., Barst R.J. Direct quantitation of right and left ventricular volumes with nuclear magnetic resonance imaging in patients with primary pulmonary hypertension. // J. Am. Coll. Cardiol. 1988. -Vol.9.- p.529.-33.
- Brenner O. Pathology of hypertensive pulmonary vascular disease. //Circulation.-1935. Vol.18: 533−547.
- Butt Y., Higenbottam T. New therapies for primary pulmonary hypertension. // Chest. 1994. — Vol. 105(Sappl.). — p.21S — 25S.
- Cantor W.J., Harrison D.A., Moussadji J.S., Connelly M.S. Webb G.D. I. iu P. McLaughlin P.R., Siu S.C. Determinants of survival and length of survival in adults with Eisenmenger syndrome. // Am. J. Cardiol. 1999. — Vol.84. -p.677−81.
- Castaneda A.R. Zamora R. Nicoloff D.M. et al. High pressure ventricular septal defect: surgical results of closure througt the right atrium. ' Ann. I horac. Surg. 1971, — Vol.12, -p.29.
- Charters A.D., Baker W. Primary pulmonary hypertension of unusually long duration. // Br. Heart J.- 1970, — Vol.32.- p. 130−3.
- Cherian G., Abraham M.T., Uthaman C.B., Sukumar L.P., Krishnaswami S. Bhakaviziam A. Primary pulmonary hypertension. // Arq. Bras. Cardiol.- 1982 -Vol.38.- p.311- 18.
- Choong C.Y., Herrmann H.C., Weyman A.E. Preload dependence of Doppler -derived indexes of left ventricular diastolic function in humans. // J. Am. Coll. Cardiol. 1987. — Vol.10. — p.800.
- Clarkson P.M., Frye R.L., Dushane J.W., Burcheu H.B., Wood E.H., Weiman W.H. Prognosis of patients with ventricular septal defect and severe pulmonary vascular obstructive disease. // Circulation. 1968. — Vol.38. — p. 129−35.
- Cohen M.L., Kronzon I. Adverse hemodynamic effects of phentolamine in primary pulmonary hypertension. // Ann. Intern. Med. 1981. — Vol.95. -p.591−2.
- Conte J.V., Gaine S.P., Orens J.В., Fiocco M., Harris Т., Rubin I. J. Continuous intravenous prostacyclin as a bridge to lung transplantation. // J. Heart Lung Transplant. 1998. (in press).
- Corone S. Davido A., Lang Т., Corone P. Outcome of patients with Eisenmenger syndrome. Apropos of 62 cases followed-up for an average of 16 years. // Arch. Mai. Coeur. Vaiss. 1992. Vol.85, p. 521 — 26.
- Currie P.J., Seward J.B. Chan K-L. et al. Continuous wave Doppler determination of right ventricular pressure: a simultaneous Dcppler-catheterization study in 127 patients. // J. Am. Coll. Cardiol. 1985. — Vol.6. -p.750- 6.
- Daliento L., Somerville J., Menti L., Rizzoli G., Stone S. Eisenmenger syndrome. Factors relating to deterioration and death. // Eur. Heart J.- 1998.-Vol.19.-p.1845- 55.
- Danielsen R., Nordrehaug J.E., Vikmo H. Importance of adjusting left ventricular diastolic peak filling rate for heart rate. /V Am. J. Cardiol. 1998. -Vol.61.-p.489.
- De Groote P., Millaire A., Foucher-Hossein C., Nugue O., Marchandise X., Ducloux G., Lablanche J. Right ventricular ejection fraction is an independent predictor of survival in patients with moderate heart failure. //JACC Vol.32: 948−54, 1998.
- Dent C.L., Perez Fontan J.J. Long-term for pulmonary hypertension in children. //Curr. Opin. Pediatr.- 1999, — Vol.11(3).- p. 218- 22.
- Di Salvo Т.О., Mathier M., S migran M.J., Dec G.W. Preserved right ventricular ejection fraction predicts exercise capacity and survival in advanced heart failure. // J. Am. Coll. Cardiol. 1995. — Vol.25. — p. 1143- 53.
- Dittrich H.C., Chow L.C., Nicod P.H. Early improvement in left ventricular diastolic function after relief of chronic right ventricular pressure overload. Circulation. Vol.80(4). — p.823−30.
- Downes T.R., Nomeir A.-M., Stewart K., Mumma M., Kerensky R., Little W.C. Effect of alteration in loading conditions on both normal and abnormal patterns of left ventricular filling in healthy individuals. // Am. J. Cardiol. -1990.-Vol.65.-p.377.
- Edwards W.D., Edwards J.E. Clinical primary pulmonary hypertension. Three pathologic types. // Circulation. 1977. — Vol.56. — p.884- 9.
- Eisenmenger V. Die angeborenens Defect der kammerschieidewand des Herzen. // Z Klin Med Suppl 1897. Vol. 32. — p. l- 28.
- Eysmann S.B., Palevsky H.I., Reichek N., Hackney K., Douglas P. S. Two-dimensional and Doppler-echocardiographic and cardiac catheterization correlates of survival in primary pulmonary hypertension. // Circulation -1989, — Vol. 80.-p.353- 60.
- Fetkovska N., Jakubovska Z., Oravkova J. Treatment of hypertension with calcium antagonists and aspirin: effects on 24- h platelet activity. // Am. J. Hypert. 1993. — Vol.6 (Suppl.). — p.98S- 101S.
- Fraser K.L., Tullis D.E., Sasson Z., Hyland R.H., Thomley K.S., Hanly P.J. Pulmonary hypertension and cardiac function in adult cystic fibrosis. //Chest.-1999.-Vol. 115, — p.1321−1328.
- Fremes S.E., Patterson G.A., Williams W.G. et al. Single lung transplantation and closure of patent ductus arteriosus for Eisenmenger’s syndrome, и J. Thorac. Cardiovasc. Surg. 1990. — Vol.100. — p. l — 5.
- Fried R. Falkowski G., Newberger J., Burakovski V. et al. Pulmonary arterial changes in patients with ventricular septal defects and severe pulmonary hypertension. // Pediatr. Cardiol. 1986. — Vol.7(3). — p. 147.
- Frist W.H., Carmichael L.C., Loyd J.E. et al. Transplantation for pulmonary hypertension. //Transplant. Proc. 1993. — Vol.25, p. l 159- 61.
- Fruzier S.K. et al. Diagnosing and treating primary pulmonary hypertension. // Nurse Pract.- 1999, — Vol. 24(9).- p. 18, 21−2, 25−6 passim., quiz. 42−3.
- Fujinami M., Morimotos S., Nishikawa T. Primary pulmonary hypertension. Study of eight autopsy cases. // Acta. Pathol. Jpn. 1987. — Vol.37, p.401 — 12.
- Fuster V., Giuliani E.R., Brandenburg R.O., Weidman W.H., Edwards W. I). The natural history of idiopathic pulmonary hypertension (abstract). // Am. J. Cardiol.- 1981, — Vol.47.- p.422.
- Fuster V., Steele P.M., Edwards W.D., Gersh B.J., McGoon M.D., Frye R.L. Primary pulmonary hypertension: natural history and the importance of thrombosis. Circulation- 1984, — Vol. 70.- p.580- 86.
- Fuster V., Steele P.M., Edwards W.D., Gersh B.J., McGoon M.D., h>e R.L. Primary pulmonary hypertension: natural history and the importance of thrombosis. // Circulation. 1984. — Vol.70. — p.580- 7.
- Gaine S.P., Rubin L.J. Medical and surgical treatment options for pulmonary hypertension. // Am. J. Med. Sci. 1998. — Vol.315(3). — p. 179−84.
- Gaine S.P., Rubin L.J. Primary pulmonary hypertension published erratum appears in Lancet 1999 Jan.2- 353(9146):74. // Lancet. 1998. — Aug.29. -352(9129).-p.719−25.
- Garcia M.J., Thomas J.D., Klein A.L. New doppler echocardiography applications for the stud) of diastolic function. J. Am. Coll. Cardiol. 1998 Vol.32. p.865- 75.
- Gibson D.G. Ventricular function. In: Anderson R.H., Macartney F.J., Shinebourne E.A., Tynan M., editors. Paediatric Cardiology. London: Churchill Livingstone 1987. — p. 159 — 79.
- Glanville A.R., Burke C.M., Theodore J., Robin E.D. Primary pulmonary hypertension: length of survival in patients referred for heart-lung transplantation. // Chest. 1987. — Vol.91. — p.675- 81.
- Goodman D.J., Harrison D.C., Popp R.L. Echocardiography features of primary pulmonary hypertension. // Am. J. Cardiol.- 1974.-Vol.33.-p.438- 43.
- Hallidie-Smith K.A., Goodwin J.F. The Eisenmenger syndrome. // Prog. Cardiol. 1974. — Vol.3. — p.211−25.
- Hamer H.P.M., Takens B.L., Posma J.L., Lie K.I. Noninvasive measurement of right ventricular systolic pressure by combined color-coded and continuous-wave Doppler ultrasound. // Am. J. Cardiol. 1988. — Vol.61. — p.668- 71.
- Harasawa M., Oosaki G., Takishima Т., Haga Т., Satake Т., Sagawa Y., Moriyama K" Nagano J. Primary pulmonary hypertension in Japan (in Japanese). Nihonkyoburinsho.- 1979, — Vol.38.- p.24−30.
- Hatano S., Strasser T. Primary pulmonary hypertension. Report on a WHO Meeting, Geneva, 15−17 Oct. 1973, Geneva. // World Health Organisation, 1975.
- Hatle L., Angelsen B. Doppler ultrasound in cardiology: physical principles and clinical applications. ed 2, Lea and Febiger, Philadelphia 1985. p.306.
- Hat!e L., Angelsen B.A.J., Tromsdal A. Noninvasive estimation of pulmonary artery systolic pressure with Doppler ultrasound. // Br. Heart J. 1981. -Vol.45. — p. 157- 65.
- Higenbottam T.W., Wells F., Wheeldon D., Wallwork J. Long-term treatment of primary pulmonary hypertension with continuous intravenous epoprostenol (prostacyclin). // Lancet. 1984. — Vol.1. — p. 1046- 7.
- Hoit B.D., Walsh R.A. Diastolic function in hypertensive heart disease. In: Gaasch W.H., LeWinter M., editors. Left Ventricular Diastolic Dysfunction and Heart Failure. // Philadelphia: Lea and Febiger 1994. p. 354- 72
- Hopkins W.E., Ochoa L.L., Richardson G.W., Trulock E.P. Comparison of the hemodynamics and survival of adults with severe primary pulmonary hypertension or Eisenmenger syndrome. // J. Heart Lung Transplant. 1996.-Vol. 15.-p.100- 5.
- Hopkins W.E., Waggoner A.D. Right and left ventricular area and function determined by two-dimensional echocardiography in adults with the Eisenmenger syndrome from a variety of congenital anomalies. // Am. J. Cardiol. 1993, — Vol. 12.- p.90−4.
- Hopkins W.E., Waggoner A.D., Gussak H. Quantitative ultrasonic tissue characterization of myocardium in cyanotic adults with an unrepaired congenital heart defect. // Am. J. Cardiol.- 1994, — Vol. 74 p. 930−4.
- Hughes J.D., Rubin L.J. Primary pulmonary hypertension: an analysis of 28 cases and a review of the literature. I1 Medicine 1986.- Vol. 65.- p.56- 72.
- Iwase M., Nagata K., Izawa H., Yokota M., Kamiha: a S., Inagaki H., Saito H. Age related changes in left and right ventricular filling velocity profiles and their relationship in normal subjects. //Am. Heart J. Vol. 126: 419−426, 1993.
- Janz R.F. Estimation of local myocardial stress. // Am. J. Physiol.- 1982.-Vol. 242, — H875−81.
- Jessup M., Sutton M.S.J., Weber K.T., Janicki J.S. The effect of chronic-pulmonary hypertension on left ventricular si/e, function, and interventricular septal motion. // Am. Heart J. 1987. — Vol.1 13. — p. 1 1 14- 22.
- Jones D.K., Higenbottam T.W., Wallwork J. Treatment of primary pulmonary hypertension with intravenous epoprostenol (prostacyclin). // Br. Heart J. 1987. — Vol.57. — p.270- 8.
- Kaiser L.R., Cooper J.D. The current status of lung transplantation. U Adv. Surg. 1992. — Vol.25. — p.259- 307.
- Kanemoto N. Natural history of pulmonary hemodynamics in primary pulmonary hypertension. // Am. Heart J.- 1987.- Vol. 114.- p.407- 13.
- Kanemoto N. Primary pulmonary hypertension: a review and report of two cases. // Asian. Med. J.- 1974.- Vol.17.- p.79- 124.
- Kanemoto N., Sasamoto H. Pulmonary hemodynamics in primary pulmonary hypertension. // Jpn. Heart J. 1979.- Vol. 20, — p. 395−405.
- Kanjuh V.J., Sellers R.D., Edwards J.E. Pulmonary vascular plexiform leasion. // Arch. Pathol. 1964. — Vol.78. — p.513- 22.
- Kapusta L., Thijssen J.M., Cuypers M.H., Peer P.G., Daniels O. Assessment of myocardial velocities in healthy children using tissue Doppler imaging. // Ultrasound Med. Biol. 2000. — Vol.26(2). — p.229- 37.
- Kitabatake A., Inoue M., Asao M., Masuyma I. Ianoiichi J., Morita I. Mishima M., Uematsu M. et al. Noninvasive evaluation of pulmonary hypertension by a pulsed Doppler technique. // Circulation 1983. — Vol.68(2). — p.302- 9.
- Kohama A., Tanouchi J., Ishihara K., Hori M" Kitabatake A., Kamada D. Pathological involvements of left ventricle in chronic cor pulmonale. II). Am. Coll. Cardiol. Vol. 13: 151 A, 1989.
- Kramer M.R., Valantine H.A., Marshall S.E., Starnes V.A., Theodore J. Recovery of the right ventricle after single-lung transplantation in pulmonary hypertension. // Am. J. Cardiol.- 1994, — Vol.73.- p.493- 500.
- Kuo L.C., Quinones M.A., Rokey R. et al. Quantification of atrial contribution to left ventricular filling by pulsed Doppler echocardiography and the effect of age in normal and diseased hearts. // Am. J. Cardiol. 1987. Vol.59, p. 1174- 8.
- Kurotobi S., Naito H., Sano «Г., Arisawa J., Matsushita Т., ГакеисЫ M., Kogaki S. Okada S. Left ventricular regional systolic motion in patients with right ventricular pressure overload. // Intern. J. Cardiol. 1998. — Vol.67. -p.55- 63.
- Lahiri A., Rodrigues F.A., Carboni G.P., Raftery F.B. Effects of long-term treatment with calcium antagonists on left ventricular diastolic function in stable angina and heart failure. //Circulation -1990.-Vol.81 .-Suppl.III.-p. 130−8.
- Levine R.A., Gibson T.C., Aretz Т., Gillam L.D., King M.F., Guver D.F. Echocardiographic measurement of right ventricular volume. II Circulation -1984. Vol. 69. — p. 497- 505.
- Levine S.M., Gibbons W.J., Bryan C.L. Single lung transplantation for primary pulmonary hypertension. // Chest. 1990. — Vol.98. — p. 1107- 15.
- Lewis B.S., Gotsman M.S. // Am. Heart J. Ю86. — Vol.99. — p. 101.
- Mahan G., Dabestani F., Gardin J. et al. Estimation of pulmonary artery pressure by pulsed Doppler echocardiography. // Circulation 1983. — Vol.68 (Suppl III).-p.302- 308.
- Marangoni S., Scalvini S., Schena M., Vitacca M., Quadri A., Levi G. Right ventricular diastolic function in chronic obstructive lung disease. I ur. Respir J. 1992, — Vol.5.- p. 438- 43.
- McLaughlin V.V., Rich S. Pulmonary hypertension advances in medical and surgical interventions. // J. Heart Lung Transplant. — Vol. 17(8). — p.739−43.
- Miyatake K., Okamoto M., Kinoshita N. et al. Evaluation of tricuspid regurgitation by pulsed Doppler and two-dimensional echocardiography. // Circulation. 1982. — Vol.66. — p.777- 84.
- Myreng Y., Smiseth O.A., Risoe C. Left ventricular filling at elevated diastolic pressure: Relationship between transmitral Doppler flow velocities and atrial contribution. // Am. Heart J. 1990. — Vol.119. — p.620.
- Nihill M.R., O’Laughlin M.P., Mullins C.E. Effects of atrial septostomy in patients with terminal cor pulmonale due to pulmonary vascular disease. // Cathet. Cardiovasc. Diagn. 1991, — Vol.24.- p. 166- 72.
- Ninomiya K., Duncan W.J., Cook D.H., Olley P.M., Rowe R.D. Right ventricular ejection fraction and volumes after Mustard repair: correlation of two-dimensional echocardiograms and cineangiograms. // Am. J. Cardiol.1981, — Vol.48, -p. 317.
- Nishimura R.A., Abel M.D., Hatle L.K., „Tajik A.J. Assessment of diastolic function of the heart: background and current applications of Doppler echocardiography. // Part II: clinical studies. Mayo Clin. Proc. 1989, — Vol. 64, — p. 181- 204.
- Niwa K“ Perloff J.K., Kaplan S. Child J.S., Miner P.D. I isenmenger Syndrome in adults: ventricular septal defect, truncus arteriosus, uni ventricular heart. // J. Am. Coll. Cardiol. 1999. — Vol.34. — p.223- 32.
- Onuki Т., Nitta S. Indications for lung transplantation and its selection of the candidates in Japan. // Nippon. Rinsho. 1999. — Vol.57(9). p.2090- 4.
- Packer M., Greenberg В., Massie В., Dash H. Deleterious effects of hydralazine in patients with pulmonary hypertension. // N. Engl. J. Med.1982.-Vol.306.-p. 1326- 31.
- Packer M., Medina N., Yusher M. Adverse hemodynamic and clinical effects of calcium channel blockade in pulmonary hypertension secondary to obliterative pulmonary vascular disease. // J. Am. Coll. Cardiol. 1984. -Vol.4.-p. 890- 901.
- Palevsky H., Fishman A. The management of primary pulmonary hypertension. //JAMA. Vol.265. — p. 1014- 20.
- Panetta C., Schiller N. Evidence of patent ductus arteriosus and right-to-left shunt by finger pulse oxymetry and Doppler signals of agitated saline in abdominal aorta. // J. Am. Soc. Echocardiogr. 1999. Sept. — Vol. 12(9).-p.763- 5.
- Park В., Dittrich H.C., Polikar R., Olson L., Nicod P. Echocardiographic evidence of pericardial effusion in severe chronic pulmonary hypertension. // Am. J. Cardiol. 1989. — Vol.63. — p. 143- 45.
- Pasque M.K., Kaiser L.R., Dressier C.M. et al. Single lung transplantation for pulmonary hypertension: technical aspects and immediate hemodynamic results. //J. Thorac. Cardiovasc. Surg. 1992. — Vol.103. — p.475- 81.
- Pasque M.K., Trulock E.P., Kaiser L.R., Cooper J.D. Single lung transplantation for pulmonary hypertension: three month hemodynamic follow up.//Circulation 1991.- Vol.84. — p.2275.- 9.
- Pepi M., Tamborini G., Galli C., Barbier P., Doria 1 Bern M. A new formula for echo-Doppler estimation of right ventricular systolic pressure. // J. Am. Soc. Echocardiogr. 1994. — Vol.7. — p.20- 26.
- Perloff J.K. The clinical recognition of congenital heart disease, edn. 4. // Philadelphia: W.B. Sanders.- 1994.-p.297- 301, 402- 7, 514- 5.
- Perrone-Filardi P., Betoechi S., Giustini G., Piscoine F., Indolfi C., Salvatore M. Influence of left ventricular asynchrony on filling in coronary artery disease. // Am. J. Cardiol. 1988. — Vol.62. — p.523−7.
- Pinamonti В., Zecchin M., Di Lenarda A., Gregori D., Sinagra G., Camerini
- F. Persistence of restrictive left ventricular filling pattern in dilated cardiomyopathy: an ominous prognostic sign. // J. Am. Coll. Cardiol. 1997,-Vol. 29.-p.604- 12.
- Plotnick G.D., Kmetzo J.J., Gottdiener J.S. Effect of autonomic blockade, postural changes and isometric exercise on Doppler indexes of diastolic left ventricular function. // Am. J. Cardiol. 1991. — Vol.67. — p. 1284.
- Pohl M.S., Cooper J.D. Results of the International Registry. In: Patterson
- G.A., Couraud L., eds. Current topics in general thoracic surgery: an international series. Vol.3. — Lung transplantation. — Amsterdam: Elsevier. -1995.- Vol.24.-p.455- 65.
- Polak J., Holman L., Wynne J. Right ventricular ejection fraction: an indicator of increased mortality in patients with congestive heart failure associated with coronary artery disease. // J. Am. Coll. Cardiol.- 1983.- Vol.2,-p.217- 24.
- Pye, M.P., Pringle, S.D., and Cobbe, S.M.: Reference values and reproducibility of Doppler echocardiography in the assessment of the tricuspid valve and right ventricular diastolic function in normal subjects. // Am. J. Car. 1991. -Vol.67. — p.269.
- Rabinovitch M., Haworth S.G., Castaneda A.R. et al. Lung biopsy in congenital heart disease: A morphometric approach to pulmonary vascular disease. // Circulation. Vol.58(6) — p. 1107- 22.
- Reed K., Anderson C.F., Shenker L. Fetal echocardiography: an atlas. //New York: Alan R. Liss.- 1988.- p.32- 3.
- Ricciardi M.J., Rubenfire M. How to manage primary pulmonary hypertension. Giving hope to patients with a life-threatening illness. // Postgrad. Med.- 1999.- Vol. 105(3).- p.45- 8, 51 -6.
- Rich S. Medical treatment of primary pulmonary hypertension: a bridge to transplantation? // Am. J. Cardiol. 1995. — Vol.75. — 63A- 66A.
- Rich S., Dodin E., McLaughlin V.V. Usefulness of atrial septostomy as a treatment for primary pulmonary hypertension and guidelines for its application. // Am. J. Cardiol.- 1997, — Vol.80.- p.369−71.
- Rich S., Kaufmann E., Levy P. S. The effect of high doses of calcium-channel blockers on survival in primary pulmonary hypertension. // N. Engl. J. Med. 1992. — Vol.327. — p.76- 81.
- Rich S., Lamb W. Atrial septostomy as palliative therapy for refractory primary pulmonary hypertension. /7 Am. J. Cardiol.- 1983.- Vol.51p. 1560−1.
- Rich S., Levy P. S. Characteristics of surviving and nonsurviving patients with primary pulmonary hypertension. // Am. J. Med.- 1984.- Vol.76.- p.573−78.
- Rich S., Pietra G.G., Kieras K. Primary pulmonary hypertension. Radiographic and scintigraphic patterns of histologic subtypes. // Ann. Intern. Med. 1986. — Vol.105.- p. 499- 502.
- Rich S., Seidlitz M., Dodin E. et al. A short-term study of digoxin in patients with right ventricular dysfunction from pulmonary hypertension. Chest. (In press).
- Rihal C.S., Nishimura R.A., Hatle L.K., Bailey K.R., Tajik A.J. Systolic and diastolic dysfunction in patients with clinical diagnosis of dilated cardiomyopathy. Relation to symptoms and prognosis. // Circulation 1994.-Vol.90.-p.2772- 9.
- Rokey R., Kuo L.C., Zoghbi W.A. et al. Determination of parameters of left ventricular diastolic filling with pulsed Doppler echocardiography: comparison with cineangiography. // Circulation 1985. — Vol.71. — p.543- 50.
- Roos-Hesselink J.W., Meijboom F.J., Spitaels S.E. Eisenmenger syndrome in adults. // Ned. Tijdschr. Geneeskd.- 1999, — Vol. 143(10).- p.501- 5. /Dutch- non-english/
- Rothman A., Beltran D» Kriett J.M., Smith C" Wolf P., Jamieson S.W. Graded balloon dilation atrial septostomy as a bridge to transplantation in primary pulmonary hypertension. // Am. Heart J. 1993.- Vol.125.- p. 1763- 6.
- Rowe G.G., Castillo С.A., Maxwell G.M., Clifford J.E., Crumpton C.W. Atrial septal defect and the mechanism of shunt. // Am. Heart J.- 1961.-Vol.61.- p.369- 74.
- Rozkovec A., Montanes P., Oakley C.M. Factors that influence the outcome of primary pulmonary hypertension. // Br. Heart J. 1986. — Vol.55. — p.449−58.
- Rubin L.J., Mendoza J., Hood M. et al. Treatment of primary pulmonary hypertension with continuous intravenous prostacyclin (epoprostenol): results of a randomized trial. // Ann. Intern. Med. 1990. — Vol.112. — p.485- 91.
- Rudolph A.M. The changes in the circulation after birth. Their importance in congenital heart disease. // Circulation 1970.- Vol.41.- p.343- 59.
- Ryan Т., Petrovic O., Dillon J.C., Feigenbaum H., Conley M.J., Armstrong W.P. An echocardiographic index for separation of right ventricular volume and pressure overload. // J. Am. Coll. Cardiol. 1985. — Vol.5. — p.918- 24.
- Saha A., Balakrishnan K.G., Jaiswal P.K., Venkitachalam C.G., Tharakan J., Titus Т., Kutty R. Prognosis for patients with Eisenmenger syndrome of various aethiology. // Int. J. Cardiol. 1994. — Vol.45, p. 199−207.
- Saito A., Ueda K., Nakano H. Right ventricular volume determination by two-dimensional echocardiography. // J. Cardiogr. 1981. — II. — p. 1159.
- Shimizu Y., Uematsu M., Nakamura Ко, Yamagishi M., Miyatake K. Peak negative myocardial velocity gradient in early diastole as a noninvasive indicator of left ventricular diastolic function. // J. Am. Coll. Cardiol. 1998. -Vol.32.-p.1418- 25.
- Silverman N.H., Norman H., Hudson S. Evaluation of right ventricular volume and ejection fraction in children by two-dimensional echocardiography. //Ped.Cardiol. Vol.4: 197−204, 1983.
- Silverman N.H., Ports T.A., Snider R" Schiller N.B. Carlsson I. Ileilbron D.C. Determination of left ventricular volume in children: echocardiographic and angiographic comparisons. //Circulation Vol. 62: 548−557, 1980.
- Silverman N.H., Schmidt K.G. The current role of Doppler echocardiography in the diagnosis of heart disease in children, 'i Cardiol. Clinics. 1989. — Vol.7(2). — p.265- 73.
- Skjaerpe Т., Hatle L. Noninvasive estimation of systolic pressure in the right ventricule in patients with tricuspid regurgitation. // Eur. Heart J. 1986. -Vol.7. — p.704- 10.
- Skjaerpe Т., Hatle L. Noninvasive estimation systolic pressure in the right ventricule in patients with tricuspid regurgitation. //Eur. Heart. J. Vol. 7: 70 410, 1986.
- Somerville J. How to manage the Eisenmenger syndrome. /7 Int. J. Cardiol. 1998. Vol.63(1). — p. 1 — 8.
- Starling M.R., Crawford M.H., Sorensen S.G. A new two-dimensional echocardiographic technique for evaluating right ventricular size and performance in patients with obstructive lung disease. // Circulation 1982. -Vol.66.-p. 612.
- Starnes V.A., Lewiston N.J., Luikart H., Theodore J., Stir. son E.B., Shumway N.E. Current trends in lung transplantation: lobar transplantation and expanded use of single lungs. // J. Thorac. Cardiovasc. Surg. 1992. — Vo.104. -p. 1060−6.
- Starnes V.A., Stinson E.B., Oyer P.E. et al. Single lung trunsplantation: a new therapeutic option for patients with pulmonary hypertension. // Transplant. Proc. 1991, — Vol.23, -p. 1209- 10.
- Stevenson J.G., Kawabori I., Guntheros W.G. // J. Am. Coll. Cardiol. 1984.-Vol.4.-p. 1021- 27.
- Stojnic B.B., Brecker S.J.D., Xiao H.B., Helmy S.M., Mbaissouroum M" Gibson D.G. Left ventricular filing characteristics in pulmonary hypertension: a new mode of ventricular interaction. //Br. Heart J. Vol. 68: 16−20, 1992.
- Suarez L.D., Sciandro E.E., Llera J.J., Perosio A.M. Long-term follow-up in primary pulmonary hypertension. // Br. Heart J.- 1979, — Vol. 41.- p.702- 8.
- Swan P., Tibbals J., Duncan A. Prostaglandin El in primary pulmonary hypertension. //Critical Care Med. 1986. — Vol.14. — p. 72- 3.
- Trell E. Benign, idiopatnic pulmonary hypertension: two further cases of unusually long duration. // Acta. Med. Scand.- 1973.- Vol. 193.- p. 137−43.
- Turkevich D., Groves B.M., Micco A., Trapp J.A., Reeves J.T. Early partial systolic closure of the pulmonic valve relates to severity of pulmonary hypertension. // Am. Heart J. 1988. Vol.115. — p.409.
- Voelkel N., Reeves J.T.: Primary pulmonary hypertension, in Moser K.M. (ed): Pulmonary Vascular Diseases, New York, Marcel Dekker.- 1979.-Vol. 14.- p. 573- 629.
- Vongpatanasin W., Brickner M.E., Hillis L .D., Lange R.A. I he Eisenmenger syndrome in adults. // Ann. Intern. Med. 1998. — Vol. 128(9). -p.745- 55.
- Wagenvoort C.A. Morphological substrate for the rerersibility of pulmonary hypertension. // Eur. Heart. J. 1988. — Vol.9. — p.7 — 12.
- Wagenvoort C.A., Mulder P.G.H. Thrombotic lesions in primary plexogenie arteriopathy. // Chest. 1993. — Vol.103. — p.844- 9.
- Wagenvoort C.A., Wagenvoort N., Takahashi T. Pulmonary veno-occlusive disease: involvement of the pulmonary arteries and review of the literature. // Hum. Pathol. 1985. — Vol. 16. — p. 1033- 41.
- Walcott G., Burchell H.B., Brown A.L.: Primary pulmonary hypertension. 4 Am. J. Med.- 1970. Vol.49.- p.70- 79.
- Weidman W.H., Bount G.Jr., DuShane J.W., Gersony W.M., Hayes C.J., Nadas A.S. The Joint Study on the Natural History of Congenital Heart Defects. // Clinical course in ventricular septal defect. // Circulation. 1977. -Vol.56(suppl). — I — p.56−79.
- Wertheimer M., Mailer J.H., Castaneda A.R. Pulmonary hypertension and congenital heart disease. // Ann. Thorac. Surg. 1973. — Vol.16. N.4. — p.416−28.
- Weyman A.E. Normall cross sectional echocardiography measurements. In Weyman A.E., editor. // Principles and practice of echocardiography. 2nd ed Philadelphia: Lea & Febiger. — 1994. — p. 1293.
- Wood P. The Eisenmenger syndrome or pulmonary hypertension with reversed central shunt. // Br. Med. J. 1958.- Vol.2.- p.701- 9.
- Wood P. The Eisenmenger syndrome or pulmonary hypertension with reversed central shunt (The Croonbn Lectures). // Br. Med. J.-l958.-Vol. 2.-p.701−9,755−62.
- Xie G-Y., Berk M R, Smith M.D., Gurley J.C., DeMaria A.N. Prognostic value of Doppler transmitra! flow patterns in patients with congestive heart failure. //J. Am. Coll. Cardiol. 1994, — Vol. 24, — p. 132- 9.
- Yock P.G., Popp R.L. Non-invasive estimation of right ventricular systolic pressure by Doppler ultrasound in patients with tricispid regurgitation. // Circulation 1984. — Vol.70. — p.657.
- Yu C.M., Sanderson J.E., Skiva Chan, Hung Y. Г., Woo K.S. Right ventricular diastolic dysfunction in heart failure. //Circulation Vol. 93: 15 091 514, 1996.
- Yuong D., Mark H. Fate of the patient with Eisenmenger syndrome. /7 Am. J. Cardiol. 1971. — Vol.28. — p.658−69.