Ранняя диагностика и значение кардиоваскулярных нарушений и мышечных изменений при синдроме Марфана у детей
Диссертация
Научная новизна. Выявлены особенности индекса соотношения нижнего сегмента тела к верхнему как одному из наиболее существенных признаков долихостеномелии в разных популяциях: у азиатов (на примере казахов) и европеоидов. Отмечено, что нижний сегмент тела у европеоидов преобладает на верхним, у азиатов это преобладание выражено меньше. Арпобирован новый признак долихостеномелии: преобладание… Читать ещё >
Содержание
- ГЛАВА I. Обзор литературы
- ГЛАВА II. Материал и методы исследования
- ГЛАВА III. Результаты собственных исследований
- 3. 1. Итоги общеклинического исследования
- 3. 2. Итоги кардиологического обследования
- ГЛАВА IV.
- Заключение
- ВЫВОДЫ 67 ПРАКТИЧЕСКИЕ РЕКОМЕНДАЦИИ
- СПИСОК ИСПОЛЬЗОВАННОЙ ЛИТЕРАТУРЫ
- СПИСОК УСЛОВНЫХ СОКРАЩЕНИЙ аУд, а/р Аутосомно-доминантный, аутосомно-рецессивный
- ВП Вызванные потенциалы
- СМ Синдром Марфана сэд Синдром Элерса-Данлоса эмг Электромиография ээг Электроэнцефалограмма
- BMP bone morfogenic protein
- GDF growth and differentiation factor
- I. Q Индекс интеллектуальности
- TGF-b Трансформирующий фактор роста (
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